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Dermatol Clin. Jul;11(3) Epidermolysis bullosa acquisita and bullous systemic lupus erythematosus. Diseases of autoimmunity to type VII collagen. Bullous Systemic Lupus Erythematosus (BSLE) is a rare manifestation of . (BP), inflammatory variant of epidermolysis bullosa acquisita (EBA), and linear IgA. However, unlike epidermolysis bullosa acquisita, bullous systemic lupus erythematosus tends to respond dramatically to treatment with.

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As seen in our case, BSLE developing with or prior to features of SLE can present a diagnostic dilemma; hence, other subepidermal vesicobullous disorders need to be ruled out.

Understanding the epidemiology and progression of systemic lupus erythematosus. Ann Intern Med,pp. J Invest Dermatol, 84pp. Nil Conflict of Interest: Se continuar a navegar, consideramos que aceita o seu uso.

Bullous Systemic Lupus Erythematosus

J Dermatol, 21pp. Semin Arthritis Rheum, 21pp. Br J Dermatol,pp. J Invest Dermatol, 81pp. Si continua navegando, consideramos que acepta su uso.

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Lupus ampolloso: un verdadero reto diagnóstico y terapéutico | Biociencias

Bullous systemic lupus erythematosus with antibodies recognizing multiple basement membrane components, bullous pemphigoid antigen1, lamini-5, laminin-6, and type VII collagen.

Hermann Pinkus memorial Lecture Other biochemical investigations were essentially normal, with no evidence of renal derangement. The geoepidemiology of systemic lupus erythematosus. Bullous eruption of systemic lupus erythematosus. The course of the disease is benign with remission reported in most of the cases within a year, including ours.


J Am Acad Dermatol, 24pp. Clinical, features, course, and outcome in patients with lateonset disease.

Cutis, 70pp. Lupus erythematosus in the s: J Invest Dermatol ; Indirect immunofluorescence in vesiculobullous eruption of systemic lupus erythematosus.

Russell’s viper venom test revealed no lupus like anticoagulant.

The blisters would rupture over days; yielding clear sometimes hemorrhagic fluid; heal over weeks; leaving behind pigmentation and occasional scarring. Our patient showed only modest improvement on steroids and antimalarials, complete response being seen only with dapsone. Enero a marzoBiociencias: J Cutan Pathol, 20pp. Yell JA, Wojnarowska F.

Bullous eruption of systemic lupus erythematosus: Our understanding of the pathology of this interesting and unique dermatologic condition has evolved with improved diagnostic criteria and clinicohistologic profiling. We described a patient who developed severe bullous lesions 14 days after high-dose systemic glucocorticoids and cyclophosphide therapies were initiated for severe SLE manifestations nephritis and alveolar hemorrhage.

Clin Exp Dermatol,pp.

Lupus Eritematoso Sistémico Bulloso en una niña de 10 años de edad. Reporte de un caso

Systemic lupus erythematosus best pract res clin Rheumatol. Vesiculobullous systemic lupus erythematosus. Int J Dermatol, 36pp. Autoimmunity to collagen VII: Bklloso to type VII collagen have heterogeneous subclass and light chain compositions and their complement-activating capacities do not correlate with the inflammatory clinical phenotype.


Lupus Eritematoso Sistémico Bulloso en una niña de 10 años de edad. Reporte de un caso

Bullous eruption of systemic lupus erythematosus Dramatic response to dapsone therapy. Case Report A year-old lady, a homemaker and mother of three, presented with largely asymptomatic vesicobullous lesions 2 months durationinvolving head and neck, upper limbs, and trunk over both photo-exposed and unexposed areas.

Dapsonetype VII collagenimmunobullous diseases. Lupus, 12pp. Arch Dermatol,pp. Lihua Duan et al. Bullous systemic lupus erythematosus with autoantibodies recognizing multiple skin basement membrane components, bullous pemphigoid antigen 1, laminin-5, laminin- 6, and type VII collagen. The patient has remained in remission without any systemic manifestations as well, over the last 1 year. Int J Dermatol ; Routine histopathology and immunoflorescence studies suggested BSLE and she responded favorably lupuss dapsone.

Efficacy and safety of belimumab in patients with active systemic lupus erythematosus: Received Nov; Accepted Jan. In addition, superficial erosions, areas of postinflammatory hyperpigmentation, and small superficial scars were noted. Susan Manzi et al. Bullous systemic lupus erythematosus: